La dilatación de la raíz de la aorta es cuando el segmento de la aorta más cercano al corazón se encuentra agrandado. Este es un problema muy serio y muy común para personas con síndrome de Marfan. Con frecuencia el tratamiento para cuando la raíz aortica alcanza cierto tamaño es una cirugía; si la raíz aortica se desgarra (disección aortica), se requiere de cirugía de emergencia.
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Shprintzen-Goldberg Syndrome Fact Sheet
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